Christopher Kubajak ,Shu Kwun Lui ,Valery Vilchez ,Tessa Cartwright ,Tessa Cartwright ,Andres Ayoob ,Eun Lee MD ,Roberto Gedaly *
Perivascular Epithelioid Cell Tumors (PEComas) are a family of rare neoplasms defined as mesenchymal tumors composed of histologically and immunohistochemically distinctive perivascular epithelioid cells. There are only few reports in the literature of PEComas of liver origin. We presented a female patient with a perivascular epitheloid cell tumor of the liver treated with laparoscopic liver resection that remains disease free after 1 year. Surgical treatment should be considered in all patients with resectable PEComas. Follow-up is indicated based on the potential for malignancy and metastasis of these lesions.